An Unusual Cause of Recurrent Chylothorax: Gorham Syndrome

Gorham syndrome, which is also called diffuse lymphangiomatosis, is characterised by excessive osteolysis due to uncontrolled lymphatic or vascular proliferation involving bones, of unknown etiology. Chylothorax may accompany Gorham syndrome in case of invasion of lymphatic vessels, or thoracic duct due to neighboring affected ribs, scapula or vertebrae. Chylothorax and vertebral invasion is seen in 1720% of patients. Even though there are many different suggested treatment modalities; Gorham syndrome with chylothorax has a very high morbidity and mortality.[1-3] This case report presents a patient with Gorham syndrome and chylothorax who was treated successfully with interferon alpha-2b.